{"slug": "jcongenital-anomalies-report", "title": "Congenital Anomalies Report 1993 \u2013 1997", "pdfUrl": "https://dhir.gov.mt/wp-content/uploads/2024/04/jcongenital_anomalies_report.pdf", "sourcePage": "https://dhir.gov.mt/en/resources/congenital-anomalies-reports/", "group": "Resource", "topic": "Congenital Anomalies Reports", "tables": [{"caption": "Table 1: Gender distribution of babies registered as having an anomaly 1993-1997", "header": ["", "Total births", "Births registered as having an anomaly", "Proportion of total births with anomaly/1000"], "rows": [["Male", "12731", "482", "37.8"], ["Female", "11777", "418", "35.4"], ["Indeterminate sex", "2", "2", "-"], ["Total", "24510", "902", "36.8"]]}, {"caption": "Table 2: Average maternal age(years)", "header": ["", "Average maternal age(years)"], "rows": [["Deliveries of babies with congenital anomalies(excluding chromosomal)", "29"], ["Deliveries of babies with chromosomal anomalies", "35*"], ["All deliveries", "29"]]}, {"caption": "Table 3: 1997 according to the group/system(s) affected", "header": ["Defect Sub Group *", "System(s) affected", "1993 1994 1995 1996 1997", "", "", "", "", "1993-97", "", ""], "rows": [["Defect Sub Group *", "System(s) affected", "", "", "", "", "", "No.", "Prev./1000 births", "Rel. Freq.%"], ["01-04", "Nervous system anomalies", "14", "20", "16", "14", "12", "76", "31.0", "5.6"], ["05-06", "Ear and Eye anomalies", "6", "9", "11", "9", "9", "44", "18.0", "3.3"], ["07-09", "Cardiac defects", "69", "102", "81", "111", "107", "470", "191.8", "34.7"], ["10", "Respiratory system defects", "3", "9", "4", "3", "5", "24", "9.8", "1.8"], ["11", "Cleft lip and palate", "13", "12", "12", "9", "11", "57", "23.3", "4.2"], ["12-14", "Digestive system anomalies", "8", "13", "12", "11", "18", "62", "25.3", "4.6"], ["15-16", "External genital anomalies", "19", "11", "13", "11", "16", "70", "33.5", "5.2"], ["17-19", "Internal urogenital anomalies", "15", "23", "14", "15", "15", "82", "28.6", "6.1"], ["20-23", "Limb defects", "33", "40", "53", "24", "35", "185", "75.5", "13.7"], ["25-29", "Musculoskeletal defects", "17", "21", "11", "17", "21", "87", "35.5", "6.4"], ["30-31", "Skin and Integement", "13", "10", "9", "6", "9", "47", "19.2", "3.5"], ["32-33", "Chromosomal anomalies", "17", "8", "14", "12", "9", "60", "24.5", "4.4"], ["34", "Metabolic defects", "5", "4", "7", "3", "6", "25", "10.2", "1.8"], ["34", "Others", "12", "13", "12", "15", "9", "61", "24.9", "4.5"], ["", "Total", "244", "295", "269", "260", "282", "1350", "552.0", "100"]]}, {"caption": "Table 4: Year by All babies, Babies registered with anomalies", "header": ["Year", "All babies*", "", "", "Babies registered with anomalies", "", ""], "rows": [["", "Live births", "Fetal deaths", "Total", "Live births", "Fetal deaths", "Total"], ["1993", "5147", "25", "5172", "159", "4", "163"], ["1994", "4826", "37", "4863", "179", "8", "187"], ["1995", "4613", "20", "4633", "182", "1", "183"], ["1996", "4944", "34", "4978", "161", "5", "166"], ["1997", "4835", "29", "4864", "199", "4", "203"], ["1993-97", "24365", "145", "24510", "880", "22", "902"]]}, {"caption": "Table 5: Proportion of fetal deaths with a congenital anomaly recorded as underlying cause of", "header": ["", "1993", "1994", "1995", "1996", "1997", "1993-97"], "rows": [["Fetal deaths*", "25", "37", "20", "34", "29", "145"], ["No. fetal deaths attributed to congenital anomalies*", "1", "4", "0", "5", "3", "13"], ["Percentage(%)", "4.0", "10.8", "0.0", "14.7", "10.3", "8.9"]]}, {"caption": "Table 6: Proportion of babies dying with a congenital anomaly recorded as underlying cause of", "header": ["", "1993", "1994", "1995", "1996", "1997", "1993-97"], "rows": [["All deaths birth to 1 wk*", "24", "29", "29", "38", "21", "141"], ["No. of these deaths due to congenital anomalies*", "12", "8", "9", "8", "9", "46"], ["Percentage(%)", "50.0", "27.6", "31.0", "21.1", "42.9", "32.6"]]}, {"caption": "Table 7: Proportion of babies dying with a congenital anomaly recorded as underlying cause of", "header": ["", "1993", "1994", "1995", "1996", "1997", "1993-97"], "rows": [["All deaths 1 wk to 1 yr*", "19", "15", "12", "15", "10", "71"], ["No. of these deaths due to congenital anomalies*", "7", "7", "4", "7", "4", "29"], ["Percentage(%)", "36.8", "46.7", "33.3", "46.7", "40.0", "40.8"]]}, {"caption": "Table 8: ICD-9Code by Diagnostic category, Year", "header": ["ICD-9Code", "Diagnostic category", "Year", "", "", "", "", ""], "rows": [["ICD-9Code", "Diagnostic category", "1993", "1994", "1995", "1996", "1997", "93-97"], ["", "I Single anomaly", "107", "130", "130", "95", "145", "607"], ["7400-7420", "-neural tube defect", "4", "6", "3", "1", "2", "16"], ["7421-7429", "-other central nervous system", "1", "9", "3", "2", "0", "15"], ["7430-7449", "-eye, ear, face and neck", "2", "6", "4", "9", "4", "25"], ["7450-7479", "-heart and circulatory system", "41", "46", "52", "42", "63", "244"], ["7480-7489", "-respiratory system", "1", "4", "2", "1", "3", "11"], ["7490-7493", "-oral clefts", "9", "7", "10", "4", "7", "37"], ["7500-7519", "-digestive system", "5", "11", "6", "4", "12", "38"], ["7520-7529", "-genital organs", "15", "5", "5", "5", "12", "42"], ["7530-7539", "-urinary system", "3", "14", "7", "3", "4", "31"], ["7540-7569", "-musculoskeletal anomalies", "13", "16", "29", "16", "22", "96"], ["7570-7579", "-skin &amp; integement", "5", "3", "3", "0", "7", "18"], ["", "-others", "8", "3", "6", "8", "9", "34"], ["", "II Syndromes", "29", "16", "21", "20", "16", "102"], ["7580-7589", "-chromosomal", "17", "8", "14", "12", "9", "60"], ["", "-other syndromes/sequences/associations", "12", "8", "7", "8", "7", "42"], ["", "III Multiple Anomalies", "27", "41", "32", "51", "42", "193"], ["", "-multiple anomalies of one system", "17", "18", "10", "32", "16", "93"], ["", "-multiple cardiovascular", "9", "15", "7", "26", "13", "70"], ["", "-multiple musculoskeletal", "3", "3", "2", "1", "1", "10"], ["", "-multiple anomalies of different systems", "10", "23", "22", "19", "26", "100"]]}, {"caption": "Table 9: Distribution of babies according to time of diagnosis", "header": ["Time of diagnosis", "1993", "1994", "1995", "1996", "1997", "93-97", "%"], "rows": [["Pre-natally", "13", "24", "11", "19", "85", "92", "10"], ["At birth", "86", "87", "99", "65", "35", "422", "47"], ["Within first week of life", "15", "20", "30", "35", "16", "135", "15"], ["1 week to 1 month", "19", "27", "16", "12", "41", "90", "10"], ["1 month to 1 year", "29", "26", "24", "30", "25", "150", "17"], ["Uncertain", "1", "3", "3", "5", "1", "13", "1.4"], ["Total", "163", "187", "183", "166", "203", "902", "100"]]}, {"caption": "Table 10: First source of Information, 1993\u20131997", "header": ["First source of Information", "1993", "1994", "1995", "1996", "1997", "93-97", "%"], "rows": [["Active data collection from maternity wards &amp; SCBU", "105", "99", "81", "11", "81", "377", "42"], ["Doctors&#x27; notification", "1", "2", "2", "6", "5", "16", "2"], ["Death Register/Postmortem", "3", "2", "4", "16", "6", "31", "3"], ["Cardiac Lab records&amp; Congenital heart disease reg", "23", "27", "33", "48", "78", "209", "23"], ["Maternity systems database", "0", "1", "34", "70", "10", "115", "13"], ["HAA", "1", "10", "14", "6", "11", "42", "5"], ["Genetics clinic", "5", "3", "6", "4", "2", "20", "2"], ["SLH operations register", "0", "0", "2", "3", "6", "11", "1"], ["Others", "4", "4", "4", "2", "4", "18", "2"], ["Unknown", "21", "39", "3", "0", "0", "63", "7"], ["Total", "163", "187", "183", "166", "203", "902", "100"]]}, {"caption": "Table 11: Distribution of babies with anomaly (livebirths and fetal deaths) by sex (1993-97)", "header": ["Sex", "Total number of babies with anomalies(Prevalence per 1000 births)", "", "", "", "", "", ""], "rows": [["Sex", "1993", "1994", "1995", "1996", "1997", "93-97", ""], ["Males", "90(33.5)", "95(38.0)", "108(44.7)", "78(30.3)", "111(43.3)", "482(37.9)", ""], ["Females", "73(29.4)", "91(38.5)", "75(33.8)", "88(36.6)", "91(39.5)", "418(35.5)", ""], ["Indeterminate", "-", "1", "-", "-", "1", "2", ""], ["Total", "163(31.5)", "187(38.4)", "183(39.5)", "166(33.3)", "203(41.7)", "902(36.8)", ""]]}, {"caption": "Table 12: Distribution of all babies with congenital anomalies according to maternal age", "header": ["Maternal age(yrs)", "Total number of babies with anomalies(Prevalence per 1000 births)", "", "", "", "", ""], "rows": [["Maternal age(yrs)", "1993", "1994", "1995", "1996", "1997", "93-97"], ["&lt;20", "11(62.1)", "5(32.9)", "10(69.9)", "5(20.9)", "9(36.6)", "40(41.8)"], ["20-24", "21(20.6)", "41(41.8)", "33(37.7)", "25(25.6)", "43(39.9)", "163(33.0)"], ["25-29", "53(28.9)", "49(29.3)", "66(40.3)", "64(36.3)", "73(43.7)", "305(35.5)"], ["30-34", "42(30.2)", "54(39.7)", "49(37.8)", "44(34.4)", "48(41.2)", "237(36.5)"], ["35-39", "28(45.7)", "28(48.9)", "20(35.8)", "22(37.9)", "26(44.4)", "124(42.6)"], ["40-44", "8(62.5)", "10(86.2)", "5(42.7)", "6(47.6)", "4(34.8)", "33(54.8)"], ["45+", "0(n/a)", "0(n/a)", "0(n/a)", "0(n/a)", "0(n/a)", "0(n/a)"], ["Total", "163(31.5)", "187(38.4)", "183(39.5)", "166(33.3)", "203(41.7)", "902(36.8)"]]}, {"caption": "Table 13: Distribution of babies with non-chromosomal defects according to maternal age", "header": ["Maternal age(yrs)", "Total number of babies with anomalies(Prevalence per 1000 births)", "", "", "", "", ""], "rows": [["Maternal age(yrs)", "1993", "1994", "1995", "1996", "1997", "93-97"], ["&lt;20", "11(62.1)", "5(32.9)", "9(62.9)", "5(20.9)", "9(36.6)", "39(40.8)"], ["20-24", "21(20.6)", "40(40.8)", "33(37.7)", "24(24.5)", "43(39.9)", "161(32.6)"], ["25-29", "52(28.4)", "47(28.1)", "66(40.3)", "63(35.7)", "70(41.9)", "298(34.7)"], ["30-34", "37(26.6)", "53(39.0)", "41(31.7)", "41(32.1)", "46(39.5)", "218(33.6)"], ["35-39", "21(34.3)", "25(43.6)", "16(28.7)", "19(32.8)", "24(41.0)", "105(36.1)"], ["40-44", "4(31.3)", "9(77.6)", "4(34.2)", "2(15.9)", "2(17.4)", "21(34.9)"], ["45+", "0(n/a)", "0(n/a)", "0(n/a)", "0(n/a)", "0(n/a)", "0(n/a)"], ["Total", "146(28.2)", "179(36.8)", "169(36.5)", "154(30.9)", "194(39.9)", "842(34.4)"]]}, {"caption": "Table 14: Distribution of babies with chromosomal defects according to maternal age", "header": ["", "Total number of babies with anomalies(Prevalence per 1000 births)", "", "", "", "", ""], "rows": [["", "1993", "1994", "1995", "1996", "1997", "93-97"], ["&lt;20", "0(n/a)", "0(n/a)", "1(7.0)", "0(n/a)", "0(n/a)", "1(1.0)"], ["20-24", "0(n/a)", "1(1.0)", "0(n/a)", "1(1.0)", "0(n/a)", "2(0.4)"], ["25-29", "1(0.5)", "2(1.2)", "0(n/a)", "1(0.6)", "3(1.8)", "7(0.8)"], ["30-34", "5(3.6)", "1(0.7)", "8(6.2)", "3(2.3)", "2(1.7)", "19(2.9)"], ["35-39", "7(11.4)", "3(5.2)", "4(7.2)", "3(5.2)", "2(3.4)", "19(6.5)"], ["40-44", "4(31.3)", "1(8.6)", "1(8.5)", "4(31.7)", "2(17.4)", "12(19.9)"], ["45+", "0(n/a)", "0(n/a)", "0(n/a)", "0(n/a)", "0(n/a)", "0(n/a)"], ["Total", "17(3.3)", "8(1.7)", "14(3.0)", "12(2.4)", "9(1.9)", "60(2.4)"]]}, {"caption": "Table 15: Total number of babies with anomalies(Prevalence per 1000 births)", "header": ["", "Total number of babies with anomalies(Prevalence per 1000 births)", "", "", "", "", ""], "rows": [["", "1993", "1994", "1995", "1996", "1997", "93-97"], ["January", "7(17.1)", "19(43.2)", "17(43.1)", "14(32.3)", "16(40.6)", "73(35.2)"], ["February", "14(37.1)", "13(34.4)", "9(26.1)", "6(15.5)", "14(38.0)", "56(30.2)"], ["March", "17(39.0)", "8(19.6)", "9(23.8)", "13(31.7)", "24(60.6)", "71(35.0)"], ["April", "13(31.5)", "16(41.7)", "18(47.5)", "15(38.0)", "15(39.2)", "77(39.4)"], ["May", "8(18.3)", "11(29.2)", "19(49.0)", "16(42.7)", "17(48.3)", "71(36.7)"], ["June", "10(25.1)", "10(24.9)", "21(55.1)", "12(28.2)", "17(38.9)", "70(34.2)"], ["July", "18(38.5)", "26(56.5)", "16(37.4)", "16(34.2)", "18(36.9)", "94(40.6)"], ["August", "19(42.6)", "12(29.0)", "11(33.1)", "14(33.5)", "17(43.0)", "73(36.4)"], ["September", "10(22.1)", "18(42.5)", "17(40.9)", "15(35.1)", "25(61.0)", "85(39.9)"], ["October", "17(35.8)", "19(50.1)", "12(27.5)", "16(38.1)", "8(20.0)", "72(34.1)"], ["November", "20(46.8)", "24(60.9)", "14(38.6)", "9(23.7)", "17(42.9)", "84(42.8)"], ["December", "10(23.2)", "11(27.2)", "20(50.9)", "20(45.5)", "15(36.1)", "76(36.4)"], ["Total", "163(31.5)", "187(38.5)", "183(39.5)", "166(33.3)", "203(42.0)", "902(36.8)"]]}, {"caption": "Table 16: Locality by Total number of babies with anomalies(Prevalence per 1000 births)", "header": ["Locality", "Total number of babies with anomalies(Prevalence per 1000 births)", "", "", "", "", ""], "rows": [["Locality", "1993", "1994", "1995", "1996", "1997", "93-97"], ["Gozo", "13(31.4)", "14(37.1)", "10(29.1)", "15(45.9)", "15(49.0)", "67(37.9)"], ["North West", "72(27.1)", "93(36.7)", "106(43.0)", "97(36.0)", "106(39.8)", "474(36.4)"], ["West", "23(48.9)", "19(39.3)", "17(40.4)", "19(35.8)", "17(30.9)", "95(38.7)"], ["North", "20(25.3)", "29(37.2)", "37(50.3)", "33(44.9)", "28(35.4)", "147(38.3)"], ["Central", "8(28.3)", "10(41.0)", "15(54.9)", "11(37.1)", "15(49.3)", "59(42.1)"], ["Central North", "11(18.9)", "17(32.3)", "20(37.2)", "18(30.7)", "30(54.6)", "96(34.5)"], ["Central West", "10(18.8)", "18(36.1)", "17(34.0)", "16(29.4)", "16(34.3)", "77(30.3)"], ["South East", "78(37.1)", "80(40.9)", "67(36.8)", "54(27.6)", "82(43.3)", "361(37.1)"], ["Central East", "14(40.5)", "17(45.9)", "12(36.9)", "12(30.4)", "26(70.3)", "81(44.9)"], ["Harbour", "14(46.1)", "10(43.1)", "6(26.8)", "7(23.6)", "9(32.5)", "46(34.5)"], ["Central South", "10(29.6)", "11(36.5)", "13(46.9)", "7(27.5)", "7(28.6)", "48(33.9)"], ["South", "20(52.5)", "16(47.5)", "12(35.3)", "9(26.7)", "17(50.6)", "74(42.8)"], ["East", "20(27.3)", "26(36.4)", "24(36.6)", "19(28.2)", "23(34.4)", "112(32.5)"], ["Total", "163(31.5)", "187(38.5)", "183(39.5)", "166(33.3)", "203(41.7)", "902(36.8)"]]}, {"caption": "Table 17: B - Analysis Of Anomalies", "header": ["", "SEX", "1993", "1994", "1995", "1996", "1997", "93.97", "Prev/10000"], "rows": [["TOTAL BIRTHS(five and fetal deaths)", "", "", "5172", "4863", "4633", "4978", "4864", "24510"], ["ANOMALIES CLASSIFIED WITHIN THE ICD-9 CHAPTER ON CONGENITAL ANOMALIES(7400-7599)", "", "", "", "", "", "", "", ""], ["NEURAL TUBE DEFECTS(7400-7420)", "", "", "6", "7", "7", "8", "5", "33"], ["7400", "ANENCEPHALEY/EXENCEPHALEY", "M", "1", "2", "0", "1", "1", "5"], ["7400", "F", "0", "1", "1", "1", "0", "3", "1.22"], ["7401", "CRANIORACHESCHISIS(TOTAL OR PARTIAL)", "M", "0", "0", "0", "0", "0", "0.00"], ["7401", "F", "0", "0", "0", "1", "0", "1", "0.41"], ["7411", "MENINGOCELE", "M", "0", "0", "0", "0", "0", "0.00"], ["7411", "F", "0", "2", "0", "0", "0", "2", "0.82"], ["7412", "MVELOMENINGOCELE", "M", "1", "0", "3", "2", "0", "6"], ["7412", "F", "0", "0", "1", "1", "2", "4", "1.63"], ["7419", "SYNABIPIDA", "M", "1", "0", "1", "0", "0", "2"], ["7419", "F", "1", "1", "1", "0", "0", "3", "1.22"], ["7420", "CEPHALOCELE", "M", "1", "1", "0", "0", "0", "2"], ["7420", "F", "1", "0", "0", "2", "2", "5", "2.04"], ["OTHER ANOMALIES OF NERVOUS SYSTEM(7421-7429)", "", "", "8", "13", "9", "8", "8", "46"], ["7421", "MICROCEPHALY", "M", "1", "1", "0", "1", "0", "3"], ["7421", "F", "1", "2", "0", "1", "1", "8", "3.26"], ["7422", "REDUCTION DEFORMATIONS OF BRAIN", "M", "2", "1", "1", "3", "1", "8"], ["7422", "F", "0", "1", "0", "0", "3", "4", "1.63"], ["7423", "CONGENITAL HYDROCEPHALY", "M", "1", "4", "3", "0", "0", "8"], ["7423", "F", "0", "3", "3", "2", "0", "8", "3.26"], ["7424", "OTHER SPECIFIED ANOMALIES OF BRAIN", "M", "2", "0", "0", "1", "3", "1.22"], ["7424", "F", "0", "1", "0", "0", "0", "1", "0.41"], ["7425", "OTHER ANOMALIES OF SPINAL CORD", "M", "0", "0", "0", "0", "0", "0.00"], ["7425", "F", "0", "0", "1", "0", "1", "1", "0.41"], ["7428", "OTHER SPECIFIED ANOMALIES OF NERVOUS SYSTEM", "M", "0", "0", "0", "0", "0", "0.00"], ["7428", "F", "0", "0", "0", "0", "2", "2", "0.82"]]}, {"caption": "Table 18: Department of Health Information", "header": ["CODE", "TEXT", "", "SEX", "1993", "1994", "1995", "1996", "1997", "93.97", "Prev./10000"], "rows": [["CONGENITAL ANOMALIES OF EYE, EAR, FACE AND NECK (7430-7449)", "", "", "", "", "", "", "", "", "", ""], ["7430", "ANOPHTHALMUS / CRYPTOPHTHALMOS", "", "", "9", "15", "13", "14", "12", "63", "25.70"], ["", "", "M", "M", "0", "0", "0", "0", "0", "0", "0.00"], ["", "", "F", "F", "0", "1", "0", "0", "1", "2", "0.82"], ["7431", "MICROHITHALMOS / APLASIA / DYSHLA\u897f\u4e9a / HYPOPHLASIA OF EYE", "", "M", "0", "0", "0", "1", "0", "1", "0.00"], ["", "", "F", "F", "0", "0", "0", "1", "0", "0", "0.41"], ["7432", "BUFHTHALMOS", "", "M", "1", "0", "0", "0", "0", "1", "0.41"], ["", "", "F", "F", "0", "1", "0", "0", "0", "1", "0.41"], ["7434", "COLDEOMA AND OTHER ANOMALIES OF ANTERIOR SEGMENTS", "", "M", "0", "0", "0", "0", "0", "0", "0.00"], ["", "", "F", "F", "0", "0", "1", "1", "1", "2", "0.82"], ["7435", "CONGENITAL ANOMALIES OF POSTERIOR SEGMENT OF EYE-B91", "", "M", "0", "0", "0", "0", "0", "0", "0.00"], ["", "", "F", "F", "0", "0", "0", "0", "1", "1", "0.41"], ["7436", "CONGENITAL ANOMALIES OF EYELIDS, LACERNAL SYSTEM AND ORBIT", "", "M", "0", "1", "0", "1", "0", "2", "0.82"], ["", "", "F", "F", "1", "0", "1", "0", "1", "3", "1.22"], ["7438", "OTHER $PECIFIED ANOMALIES OF EYE", "", "M", "1", "0", "0", "0", "0", "1", "0.41"], ["", "", "F", "F", "0", "0", "0", "0", "0", "0", "0.00"], ["7441", "ACCESSORY AURICLE", "", "M", "1", "1", "1", "2", "2", "7", "2.86"], ["", "", "F", "F", "0", "0", "0", "0", "0", "0", "0.00"], ["7442", "OTHER $PECIFIED ANOMALIES OF EYE", "", "M", "2", "3", "2", "2", "5", "14", "5.71"], ["", "", "F", "F", "0", "1", "5", "2", "2", "8", "3.26"], ["", "", "UN", "0", "1", "0", "0", "0", "0", "1", "0.41"], ["7443", "UNSPECIFIED ANOMALIES OF EYE", "", "M", "0", "0", "0", "0", "0", "0", "0.00"], ["", "", "F", "F", "0", "1", "0", "0", "0", "1", "0.41"], ["7444", "ANOMALIES OF FIRST BRANCHAL ARCH/INCLUDING PREAURUCULAR SINUS", "", "M", "1", "1", "0", "2", "0", "4", "1.63"], ["", "", "F", "F", "0", "2", "2", "2", "0", "6", "2.45"], ["7445", "WEBBING OF NECK", "", "M", "0", "1", "0", "0", "0", "1", "0.41"], ["", "", "F", "F", "0", "1", "0", "0", "0", "1", "0.41"], ["7448", "OTHER $PECIFIED ANOMALIES OF FACE AND NECK", "", "M", "0", "1", "0", "0", "0", "1", "0.41"], ["", "", "F", "F", "0", "1", "0", "0", "0", "1", "0.41"], ["7449", "UNSPECIFIED ANOMALIES OF FACE AND NECK", "", "M", "1", "0", "1", "0", "0", "2", "0.82"], ["", "", "F", "F", "0", "0", "1", "1", "1", "2", "0.82"]]}, {"caption": "Table 17: All anomalies registered in Malta from 1993-1997 (as at December 1999)", "header": ["CODE", "TEXT", "SEX", "1993", "1994", "1995", "1996", "1997", "93-97", "Prec./10000"], "rows": [["ANOMALIES OF CARDIOVASCULAR SYSTEM (C 450-7479)", "", "", "77", "113", "85", "124", "113", "512", "208.89"], ["7450", "COMMON ARTERIAL TRUNCUS", "M", "0", "0", "0", "0", "0", "0", "0.00"], ["7450", "COMMON ARTERIAL TRUNCUS", "F", "0", "0", "0", "1", "0", "1", "0.41"], ["7451", "DISCOORDANT VENTRICULOARTERIAL/ATROVENTERICULAR CONNECTION", "M", "2", "1", "1", "1", "2", "7", "2.86"], ["7451", "DISCOORDANT VENTRICULOARTERIAL/ATROVENTERICULAR CONNECTION", "F", "0", "2", "0", "2", "0", "4", "1.63"], ["7452", "TETRALOGY OFFALLOT", "M", "1", "0", "1", "0", "3", "5", "2.04"], ["7452", "TETRALOGY OFFALLOT", "F", "1", "0", "0", "1", "1", "3", "1.22"], ["7453", "SINGLE VENTRICLE", "M", "0", "0", "0", "0", "1", "1", "0.41"], ["7453", "SINGLE VENTRICLE", "F", "0", "0", "0", "0", "0", "1", "0.00"], ["7454", "VENTRICULAR SEPTIAL DEFECT", "M", "12", "9", "17", "15", "16", "69", "28.15"], ["7454", "VENTRICULAR SEPTIAL DEFECT", "F", "12", "17", "18", "18", "20", "85", "34.68"], ["7455", "ATRIAL SEPTIAL DEFECT CG TUMOR SECUNDUM TYPE", "M", "10", "16", "14", "13", "14", "67", "27.34"], ["7455", "ATRIAL SEPTIAL DEFECT CG TUMOR SECUNDUM TYPE", "F", "11", "23", "11", "29", "30", "104", "42.43"], ["7456", "ENDOCARDIAL CUSHION DEFECT", "M", "0", "1", "1", "0", "1", "3", "1.22"], ["7456", "ENDOCARDIAL CUSHION DEFECT", "F", "3", "1", "1", "7", "0", "12", "4.90"], ["7460", "ANOMALIES OF PULMONARY VALVE", "M", "4", "7", "5", "3", "3", "22", "8.98"], ["7460", "ANOMALIES OF PULMONARY VALVE", "F", "6", "9", "4", "3", "6", "28", "11.42"], ["7461", "ANOMALIES OF TRECUSHD VALVE", "M", "1", "0", "0", "0", "0", "1", "0.41"], ["7461", "ANOMALIES OF TRECUSHD VALVE", "F", "0", "0", "0", "1", "0", "1", "0.41"], ["7462", "EES TENNS ANOMALY AND OTHER ANOMALIES OF TRECUSHD VALVE", "M", "0", "0", "1", "0", "1", "2", "0.82"], ["7462", "EES TENNS ANOMALY AND OTHER ANOMALIES OF TRECUSHD VALVE", "F", "0", "0", "0", "1", "0", "1", "0.41"], ["7463", "AORTIC VALVE ATRENIA/STENOSIS", "M", "2", "0", "1", "1", "1", "5", "2.04"], ["7463", "AORTIC VALVE ATRENIA/STENOSIS", "F", "0", "0", "1", "0", "0", "1", "0.41"], ["7464", "OTHER ANOMALIES OF AORTIC VALVE", "M", "1", "1", "0", "0", "0", "2", "0.82"], ["7464", "OTHER ANOMALIES OF AORTIC VALVE", "F", "0", "1", "0", "0", "0", "1", "0.41"], ["7465", "MITRAL VALVE ATRENIA&amp;TENOSIS", "M", "0", "0", "0", "0", "0", "0", "0.00"], ["7465", "MITRAL VALVE ATRENIA&amp;TENOSIS", "F", "0", "1", "0", "0", "0", "1", "0.41"], ["7466", "OTHER ANOMALIES OF MITRAL VALVE", "M", "0", "0", "0", "0", "0", "0", "0.00"], ["7466", "OTHER ANOMALIES OF MITRAL VALVE", "F", "1", "0", "0", "1", "0", "2", "0.82"], ["7467", "HYPOPLASTIC LEFT HEART SYNDROME", "M", "1", "0", "2", "0", "0", "3", "1.22"], ["7467", "HYPOPLASTIC LEFT HEART SYNDROME", "F", "0", "0", "0", "0", "0", "0", "0.00"]]}, {"caption": "Table 20: Department of Health Information", "header": ["CODE", "TEXT", "SEX", "1993", "1994", "1995", "1996", "1997", "93.97", "Prev./10000", ""], "rows": [["7468", "OTHER MALFORMATIONS AND ANOMALIES OF THE HEART", "M", "0", "1", "1", "3", "0", "5", "2.04", ""], ["7468", "OTHER MALFORMATIONS AND ANOMALIES OF THE HEART", "F", "0", "1", "0", "3", "0", "4", "1.63", ""], ["7470", "PATENT DUCTUS ARTERIOUSIS", "M", "2", "6", "1", "4", "4", "17", "6.94", ""], ["7470", "PATENT DUCTUS ARTERIOUSIS", "F", "1", "6", "5", "6", "3", "21", "8.57", ""], ["7471", "COARCTATION OF AORTIA", "M", "2", "3", "0", "3", "1", "9", "3.67", ""], ["7471", "COARCTATION OF AORTIA", "F", "0", "3", "0", "1", "2", "6", "2.45", ""], ["7472", "OTHER ANOMALIES OF THE AORTIA", "M", "0", "1", "0", "2", "2", "5", "2.04", ""], ["7472", "OTHER ANOMALIES OF THE AORTIA", "F", "0", "0", "0", "0", "0", "0", "0.00", ""], ["7473", "ANOMALIES OF PULMONARY ARTERY", "M", "0", "0", "0", "0", "2", "2", "0.82", ""], ["7473", "ANOMALIES OF PULMONARY ARTERY", "F", "1", "2", "0", "2", "0", "5", "2.04", ""], ["7474", "ANOMALIES OF GREAT VEINS", "M", "1", "0", "0", "0", "0", "1", "0.41", ""], ["7474", "ANOMALIES OF GREAT VEINS", "F", "1", "0", "0", "2", "0", "3", "1.22", ""], ["7479", "UNSPECIFIED ANOMALIES OF CHEULATORY SYSTEM", "M", "1", "1", "0", "1", "0", "3", "1.22", ""], ["7479", "UNSPECIFIED ANOMALIES OF CHEULATORY SYSTEM", "F", "0", "1", "0", "0", "0", "0", "0.00", ""], ["ANOMALIES OF NOSE AND RESPIRATORY SYSTEM (7480-7489)", "", "", "5", "11", "4", "3", "8", "31", "12.65", ""], ["7480", "CHOANALETRICIA/STENOSIS", "M", "0", "1", "0", "0", "3", "4", "1.63", ""], ["7480", "CHOANALETRICIA/STENOSIS", "F", "1", "0", "0", "0", "0", "1", "0.41", ""], ["7481", "OTHER ANOMALIES OF NOSE", "M", "1", "0", "0", "0", "0", "0", "0.00", ""], ["7481", "OTHER ANOMALIES OF NOSE", "F", "1", "1", "0", "0", "0", "2", "0.82", ""], ["7483", "OTHER ANOMALIES OF LARYNG, TRACHEA AND BRONCHUS+B198", "M", "0", "1", "1", "1", "1", "4", "1.63", ""], ["7483", "OTHER ANOMALIES OF LARYNG, TRACHEA AND BRONCHUS+B198", "F", "1", "3", "0", "1", "1", "6", "2.45", ""], ["7485", "AGENESIS, HYPOPLASIA AND DYSPLASIA OF LUNG", "M", "2", "1", "3", "0", "2", "8", "3.26", ""], ["7485", "AGENESIS, HYPOPLASIA AND DYSPLASIA OF LUNG", "F", "2", "0", "1", "1", "1", "4", "1.63", ""], ["7485", "AGENESIS, HYPOPLASIA AND DYSPLASIA OF LUNG", "UN", "0", "1", "0", "0", "0", "1", "0.41", ""], ["7485", "AGENESIS, HYPOPLASIA AND DYSPLASIA OF LUNG", "", "", "", "", "", "", "", "1", "0.41"], ["7488", "OTHER SPECIFIED ANOMALIES OF THE RESPRATORY SYSTEM", "M", "0", "1", "0", "0", "0", "1", "0.41", ""], ["7488", "OTHER SPECIFIED ANOMALIES OF THE RESPRATORY SYSTEM", "F", "0", "0", "0", "0", "0", "0", "0.00", ""], ["CLEFT PALATE AND CLEFT LIP (7480-7493)", "", "", "13", "12", "12", "9", "11", "57", "23.26", ""], ["7490", "CLEFT OF SECONDARY PALATE", "M", "5", "3", "3", "4", "3", "18", "7.34", ""], ["7490", "CLEFT OF SECONDARY PALATE", "F", "3", "3", "4", "3", "4", "17", "6.94", ""], ["7490", "CLEFT OF SECONDARY PALATE", "UN", "0", "1", "0", "0", "0", "1", "0.41", ""]]}, {"caption": "Table 17: All anomalies registered in Malta from 1993-1997 (as at December 1999) (2)", "header": ["CODE", "TEXT", "", "SEX", "1993", "1994", "1995", "1996", "1997", "93.97", "Prev./10000"], "rows": [["7491", "CLEFT OF PRIMARY PALATE/CLEFT LIP", "", "M", "1", "1", "2", "0", "2", "6", "2.45"], ["", "", "", "F", "1", "0", "0", "0", "0", "1", "0.41"], ["7492", "CLEFT OF PRIMARY AND SECONDARY PALATE", "", "M", "2", "3", "3", "1", "1", "10", "4.08"], ["", "", "", "F", "1", "1", "0", "1", "1", "4", "1.63"], ["ANOMALIES OF UPPER ALIMENTARY TRACT (7500-7509)", "", "", "", "7", "14", "4", "3", "15", "43", "17.54"], ["7500", "ANKYLOGLOSSIA", "", "M", "0", "0", "1", "0", "0", "1", "0.41"], ["", "", "", "F", "0", "0", "0", "0", "0", "0", "0.00"], ["7501", "OTHER ANOMALIES OF THE TONGUE", "", "M", "0", "0", "0", "0", "0", "1", "0.41"], ["", "", "", "F", "0", "0", "0", "1", "0", "1", "0.00"], ["7502", "OTHER SPECIFIED ANOMALIES OF MOUTH AND PHARYNX", "", "M", "0", "2", "0", "0", "0", "2", "0.82"], ["7503", "TRACHEO-OESPHAGEAL FESTULA, OESPHAGEAL ATREASIA AND STENOSIS", "", "M", "2", "1", "0", "0", "1", "4", "1.63"], ["", "", "", "F", "0", "1", "0", "0", "0", "1", "0.41"], ["7505", "CONGENITAL HYPERTROPHIC PYLORIC STENOSIS", "", "M", "3", "7", "3", "1", "12", "26", "10.61"], ["", "", "", "F", "0", "2", "0", "1", "1", "4", "1.63"], ["OTHER ANOMALIES OF DIGESTIVE SYSTEM (7510-7519)", "", "", "", "4", "2", "9", "9", "4", "28", "11.42"], ["7511", "ATRESIA AND STENOSIS OF SMALL INTESTINE", "", "M", "0", "0", "0", "1", "0", "1", "0.41"], ["7512", "ATRESIA STENOSIS OF LARGE INTESTINE, RECUMUM AND ANAL CANAL", "", "M", "3", "0", "3", "3", "0", "9", "3.67"], ["", "", "", "F", "0", "0", "0", "1", "0", "1", "0.41"], ["", "", "", "UN", "0", "0", "0", "0", "1", "1", "0.41"], ["7513", "HIES CHRUPINGS DISEASE AND OTHER CONG FUNCTION ALL ORDERS OF COLON", "", "M", "0", "1", "2", "3", "0", "6", "2.45"], ["7514", "ANOMALIES OF INTESTINAL FITATION AND MERENTERIC ANOMALIES", "", "M", "0", "0", "0", "0", "0", "0", "0.00"], ["7515", "OTHER ANOMALIES OF INTESTINE", "", "M", "1", "0", "0", "0", "0", "1", "0.41"], ["7516", "ANOMALIES OF GALL BLADDER, HILE DUCTS AND LIVER", "", "M", "0", "0", "1", "0", "0", "1", "0.41"]]}, {"caption": "Table 22: Department of Health Information", "header": ["CODE", "TEXT", "SEX", "1993", "1994", "1995", "1996", "1997", "93.97", "Prev.10000"], "rows": [["ANOMALIES OF CENITIAL ORGAN SYSTEM (7520-7529)", "", "", "19", "14", "14", "12", "17", "76", "31.01"], ["7520", "ANOMALIES OF OVARIES", "M", "0", "0", "0", "0", "0", "0", "0.00"], ["", "", "F", "0", "2", "0", "0", "0", "2", "0.82"], ["7523", "ANOMALIES OF UTERUS", "M", "0", "0", "0", "0", "0", "0.00", "0.00"], ["", "", "F", "0", "0", "0", "0", "1", "1", "0.41"], ["7524", "ANOMALIES OF CERVIC VAGINA AND EXTERNAL GENITALIA", "M", "0", "0", "0", "0", "0", "0", "0.00"], ["", "", "F", "2", "3", "1", "1", "1", "7", "2.86"], ["7525", "ANOMALIES OF TESTCLES", "M", "1", "3", "4", "4", "1", "13", "5.30"], ["", "", "F", "0", "0", "0", "1", "0", "1", "0.41"], ["7526", "HYPOPSADIAS / ENDSADIAS / CONGENITAL CHODEDEE", "M", "12", "2", "9", "4", "13", "40", "16.32"], ["", "", "F", "0", "0", "0", "0", "0", "0", "0.00"], ["7527", "INDETEMINATE SEXAND PSEUDOHERMAPHOIDISM", "M", "0", "0", "0", "1", "0", "1", "0.41"], ["", "", "F", "2", "0", "0", "0", "0", "2", "0.82"], ["", "", "UN", "0", "1", "0", "0", "1", "2", "0.82"], ["7528", "OTHER ANOMALIES OF MALE GENITAL TRACT", "M", "2", "3", "1", "1", "0", "7", "2.86"], ["", "", "F", "0", "0", "0", "0", "0", "0", "0.00"], ["ANOMALIES OF URINARY SYSTEM (7530-7539)", "", "", "18", "24", "14", "17", "15", "88", "35.90"], ["7530", "RENAL AGENESIS AND DYSGENESIS", "M", "2", "1", "1", "2", "0", "6", "2.45"], ["", "", "F", "0", "0", "0", "0", "1", "1", "0.41"], ["7531", "CYSTIC KIDNEY DENSE", "M", "1", "1", "3", "1", "1", "7", "2.86"], ["", "", "F", "1", "2", "0", "0", "1", "4", "1.63"], ["7532", "OBSTECTIVE DEFECTS OF RENAL PELVIS AND URETER", "M", "3", "11", "5", "7", "7", "33", "13.46"], ["", "", "F", "5", "4", "1", "0", "3", "13", "5.30"], ["", "", "UN", "0", "2", "0", "0", "0", "2", "0.82"], ["7533", "OTHER SPECIFIED ANOMALIES OF KIDNEY", "M", "1", "2", "1", "2", "1", "7", "2.86"], ["", "", "F", "2", "1", "0", "1", "1", "5", "2.04"], ["7534", "OTHER SPECIFIED ANOMALIES OF URETER", "M", "1", "0", "0", "1", "0", "2", "0.82"], ["", "", "F", "0", "0", "0", "1", "0", "1", "0.41"], ["7536", "ATRESIA &amp; OTHER CONGENITAL STENOSIS OF URETHRA &amp; ELADDER NECK", "M", "1", "0", "0", "2", "0", "3", "1.22"], ["", "", "F", "0", "0", "1", "0", "0", "1", "0.41"], ["7538", "OTHER SPECIFIED ANOMALIES OF ELADDER AND URETHRA", "M", "1", "0", "2", "0", "0", "3", "1.22"]]}, {"caption": "Table 17: All anomalies registered in Malta from 1993-1997 (as at December 1999) (3)", "header": ["CODE", "TEXT", "SEX", "1993", "1994", "1995", "1996", "1997", "93.97", "Prev.10000"], "rows": [["ANOMALIES OF MUSCULOSKELETAL SYSTEM (7540-7549)", "", "", "10", "26", "31", "12", "21", "100", "40.80"], ["7540", "CONG. MUSCULOSKELETAL DEFORMITTES OF SKDLL, FACE AND IAW", "M", "0", "5", "0", "1", "2", "8", "3.26"], ["7540", "CONG. MUSCULOSKELETAL DEFORMITTES OF SKDLL, FACE AND IAW", "F", "0", "0", "1", "0", "2", "3", "1.22"], ["7543", "CONGENTIAL DNLOCATION OF HIP", "M", "1", "0", "1", "0", "1", "3", "1.22"], ["7543", "CONGENTIAL DNLOCATION OF HIP", "F", "1", "7", "5", "1", "1", "15", "6.12"], ["7544", "CONGENTIAL GENU RECURVATUM AND BOVING OF LONG PONES OF LEG", "M", "1", "0", "2", "0", "0", "3", "1.22"], ["7544", "CONGENTIAL GENU RECURVATUM AND BOVING OF LONG PONES OF LEG", "F", "0", "1", "0", "0", "0", "1", "0.41"], ["7545", "VARUS DEFORMITTES OF FEET", "M", "2", "2", "9", "3", "5", "21", "8.57"], ["7545", "VARUS DEFORMITTES OF FEET", "F", "0", "1", "3", "3", "5", "12", "4.90"], ["7546", "VALGUS DEFORMITTES OF FEET", "M", "0", "1", "2", "0", "1", "4", "1.00"], ["7546", "VALGUS DEFORMITTES OF FEET", "F", "0", "0", "0", "0", "0", "0", "0.00"], ["7547", "OTHER DEFORMITTES OF FEET", "M", "1", "5", "4", "4", "2", "16", "6.53"], ["7547", "OTHER DEFORMITTES OF FEET", "F", "2", "3", "4", "0", "2", "11", "4.49"], ["7548", "OTHER SPECIFIED DEFORMITTES OF THORAX AND LIMES", "M", "1", "1", "0", "0", "0", "2", "0.82"], ["7548", "OTHER SPECIFIED DEFORMITTES OF THORAX AND LIMES", "F", "1", "0", "0", "0", "0", "1", "0.41"], ["ANOMALIES OF LIMITS (7550-7559)", "", "", "25", "25", "26", "16", "18", "110", "44.88"], ["7550", "POLYDACTYL / POLYSYNDACTYL HANDS AND FEET", "M", "7", "4", "7", "1", "5", "24", "9.79"], ["7550", "POLYDACTYL / POLYSYNDACTYL HANDS AND FEET", "F", "4", "5", "1", "6", "3", "19", "7.75"], ["7551", "SYNDACTYL HANDS AND FEET", "M", "1", "3", "2", "3", "2", "11", "4.49"], ["7551", "SYNDACTYL HANDS AND FEET", "F", "4", "3", "3", "0", "2", "9", "3.67"], ["7552", "REDUCTION DEFORMITTES OF UPPER LIMES", "M", "0", "2", "3", "0", "1", "6", "2.45"], ["7552", "REDUCTION DEFORMITTES OF UPPER LIMES", "F", "1", "1", "0", "0", "0", "2", "0.82"], ["7553", "REDUCTION DEFORMITTES OF LOWER LIMES", "M", "0", "0", "2", "1", "0", "3", "1.22"], ["7553", "REDUCTION DEFORMITTES OF LOWER LIMES", "F", "1", "0", "0", "0", "0", "1", "0.41"], ["7555", "OTHER ANOMALIES OF UPPER LIMB, INCLUDING SHOULDER GREDLE", "M", "1", "3", "1", "1", "1", "7", "2.86"], ["7555", "OTHER ANOMALIES OF UPPER LIMB, INCLUDING SHOULDER GREDLE", "F", "1", "2", "2", "0", "1", "6", "2.45"], ["7556", "OTHER ANOMALIES OF LOWER LIMB, INCLUDING PELVIC GREDLE", "M", "2", "2", "1", "1", "0", "6", "2.45"], ["7556", "OTHER ANOMALIES OF LOWER LIMB, INCLUDING PELVIC GREDLE", "F", "0", "1", "1", "2", "1", "5", "2.04"], ["7558", "OTHER SPECIFIED ANOMALIES OF UNSPECIFIED LIMB", "M", "1", "1", "1", "1", "1", "5", "2.04"], ["7558", "OTHER SPECIFIED ANOMALIES OF UNSPECIFIED LIMB", "F", "2", "0", "2", "0", "0", "4", "1.63"], ["7559", "UNSPECIFIED ANOMALIES OF UNSPECIFIED LIMB", "M", "0", "1", "0", "0", "0", "1", "0.41"], ["7559", "UNSPECIFIED ANOMALIES OF UNSPECIFIED LIMB", "F", "0", "0", "0", "0", "1", "1", "0.41"]]}, {"caption": "Table 24: Department of Health Information", "header": ["CODE", "TEXT", "SEX", "1993", "1994", "1995", "1996", "1997", "93.97", "Prev./10000"], "rows": [["OTHER MUSCULOSKELETAL ANOMALIES (7560-7569)", "", "", "9", "9", "9", "14", "11", "52", "21.22"], ["7560", "ANOMALIES OF SKULL AND FACE BONES", "M", "2", "1", "1", "1", "1", "6", "2.45"], ["7560", "ANOMALIES OF SPINE", "F", "0", "0", "1", "2", "2", "5", "2.04"], ["7561", "ANOMALIES OF SPINE", "M", "0", "0", "0", "0", "1", "1", "0.41"], ["7561", "O OTHER ANOMALIES OF RIES AND STERNUM", "F", "0", "1", "1", "1", "0", "3", "1.22"], ["7563", "O OTHER ANOMALIES OF RIES AND STERNUM", "M", "0", "0", "0", "0", "0", "0", "0.00"], ["7563", "CHONDRO/OSTEO CHONDRO DY STROPHY, CHONDRO/OSTEO CHONDRO DY SPLASIA", "F", "0", "0", "0", "0", "0", "1", "0.41"], ["7564", "CHONDRO/OSTEO CHONDRO DY STROPHY, CHONDRO/OSTEO CHONDRO DY SPLASIA", "M", "0", "0", "0", "0", "0", "0", "0.00"], ["7564", "OSTEOD Y STROPHIES", "F", "0", "2", "0", "0", "0", "2", "0.82"], ["7565", "OSTEOD Y STROPHIES", "M", "0", "0", "0", "0", "0", "0", "0.00"], ["7565", "ANOMALIES OF DIAPHRAEM", "F", "0", "0", "1", "1", "1", "3", "1.22"], ["7566", "ANOMALIES OF DIAPHRAEM", "M", "0", "0", "3", "1", "3", "7", "2.86"], ["7566", "ANOMALIES OF AEDOMINAL WALL", "F", "2", "3", "1", "3", "0", "8", "3.26"], ["7567", "ANOMALIES OF AEDOMINAL WALL", "M", "3", "0", "0", "3", "1", "7", "2.88"], ["7567", "UN", "F", "1", "2", "1", "1", "1", "6", "2.45"], ["7567", "O OTHER SPECIFIED ANOMALIES OF MUSCLE, TEND ON, FAScia &amp; CONNECTIVE TISSUE", "F", "0", "0", "0", "0", "1", "1", "0.41"], ["7568", "O OTHER SPECIFIED ANOMALIES OF MUSCLE, TEND ON, FAScia &amp; CONNECTIVE TISSUE", "M", "0", "0", "1", "0", "0", "1", "0.41"], ["7568", "UNSPECIFIED ANOMALIES OF MUSCULOSKELETAL SYSTEM", "F", "0", "0", "0", "0", "0", "0", "0.00"], ["CONGENITAL ANOMALIES OF INTEGUMENT (7570-7579)", "", "", "13", "10", "8", "6", "9", "46", "18.77"], ["7571", "ICHTHYOSIS CONGENITA", "M", "1", "0", "0", "0", "1", "2", "0.82"], ["7571", "DERMA TOGLYPIC ANOMALIES", "F", "1", "0", "0", "1", "0", "2", "0.82"], ["7572", "DERMA TOGLYPIC ANOMALIES", "M", "1", "2", "0", "0", "0", "3", "1.22"], ["7572", "O OTHER SPECIFIED ANOMALIES OF SKIN", "F", "0", "0", "0", "0", "0", "0", "0.00"], ["7573", "O OTHER SPECIFIED ANOMALIES OF SKIN", "M", "5", "3", "2", "2", "2", "14", "5.71"], ["7573", "SPECIFIED ANOMALIES OF HAIR", "F", "4", "4", "5", "2", "6", "21", "8.57"], ["7574", "SPECIFIED ANOMALIES OF HAIR", "M", "0", "1", "0", "0", "0", "1", "0.41"], ["7574", "SPECIFIED ANOMALIES OF HAIR", "F", "0", "0", "0", "0", "0", "0", "0.00"], ["7575", "SPECIFIED ANOMALIES OF HAIR", "M", "1", "0", "0", "0", "0", "1", "0.41"], ["7575", "SPECIFIED ANOMALIES OF HAIR", "F", "0", "0", "1", "1", "0", "2", "0.82"]]}, {"caption": "Table 17: All anomalies registered in Malta from 1993-1997 (as at December 1999) (4)", "header": ["CODE", "TEXT", "SEX", "1993", "1994", "1995", "1996", "1997", "93.97", "Prev/10000"], "rows": [["CHROMOSOMAL ANOMALIES(7580-7589)", "", "", "17", "8", "14", "12", "9", "60", "24.48"], ["7580", "DOWN SYNDROME", "M", "4", "5", "5", "2", "2", "18", "7.34"], ["", "", "F", "11", "2", "3", "6", "1", "23", "9.38"], ["7582", "EDWARD SYNDROME AND OTHER TOTAL TRISOMIES OF E GROUP", "M", "0", "0", "1", "1", "2", "4", "1.63"], ["", "", "F", "0", "1", "1", "0", "2", "4", "1.63"], ["7583", "AUTOSOMAL DELETION SYNDROMES", "M", "1", "0", "1", "0", "0", "2", "0.82"], ["", "", "F", "0", "0", "1", "1", "0", "2", "0.82"], ["7584", "BALANCED AUTOSOMAL TRANSLOCATIONS IN NORMAL INDIVIDUAL", "M", "0", "0", "1", "0", "0", "1", "0.41"], ["", "", "F", "1", "0", "1", "0", "0", "2", "0.82"], ["7585", "OTHER CONDITIONS DUE TO AUTOSOMAL ANOMALIES", "M", "0", "0", "0", "0", "0", "0", "0.00"], ["", "", "F", "0", "0", "0", "2", "0", "2", "0.82"], ["7586", "ABERRATIONS OF THE X CHROMOSOME IN THE ABSENCE OF A Y CHROMOSOME", "M", "0", "0", "0", "0", "0", "0", "0.00"], ["", "", "F", "0", "0", "0", "0", "1", "1", "0.41"], ["7589", "CONDITIONS DUE TO ANOMALY OF UNSPECIFIED CHROMOSOMES", "M", "0", "0", "0", "0", "1", "1", "0.41"], ["", "", "F", "0", "0", "0", "0", "0", "0", "0.00"], ["OTHER AND UNSPECIFIED CONGENITAL ANOMALIES", "", "", "5", "4", "3", "6", "4", "22", "8.98"], ["7591", "ANOMALIES OF ADRENAL GLAND", "M", "0", "0", "0", "0", "0", "0", "0.00"], ["", "", "F", "0", "0", "0", "1", "0", "1", "0.41"], ["7593", "SITUS INVESUS", "M", "0", "1", "0", "0", "0", "1", "0.41"], ["", "", "F", "0", "0", "0", "0", "0", "0", "0.00"], ["7596", "HAMARTOSIS NEC", "M", "0", "0", "0", "0", "0", "0", "0.00"], ["", "", "F", "1", "0", "0", "0", "0", "1", "0.41"], ["7598", "SYNDROMES AND MULTIPLE CONGENITAL ANOMALIES NEC", "M", "2", "2", "2", "2", "1", "9", "3.67"], ["", "", "F", "2", "1", "1", "3", "3", "10", "4.08"], ["OTHER ANOMALIES NOT CLASSIFIED WITHIN THE ICD 9 CHAPTER ON CONGENITAL ANOMALIES", "", "", "", "", "", "", "", "", ""], ["NEOPLASMS (1400-2399)", "", "", "1", "0", "4", "2", "2", "9", "3.67"], ["1905", "MALIGNANT NEOPLASM OF RETINA", "M", "1", "0", "1", "0", "0", "2", "0.82"], ["", "", "F", "0", "0", "0", "0", "1", "1", "0.41"]]}, {"caption": "Table 26: Department of Health Information", "header": ["CODE", "TEXT", "SEX", "1993", "1994", "1995", "1996", "1997", "93-97", "Prev/10000", ""], "rows": [["1940", "MALIGNANT NEOPLASM OF SUPRARENA GLAUD", "M", "0", "0", "1", "1", "0", "2", "0.82", ""], ["", "", "F", "0", "0", "1", "0", "0", "1", "0.41", ""], ["1991", "MALIGNANCY, UNSPECIFIED SITE", "M", "0", "0", "0", "1", "0", "1", "0.41", ""], ["", "", "F", "0", "0", "0", "0", "0", "0", "0.00", ""], ["2157", "BENIGN NEOPLASM OF CONNECTIVE TISSUE TRUNK/BACK NOS", "M", "0", "0", "0", "0", "1", "1", "0.41", ""], ["", "", "F", "0", "0", "0", "0", "0", "0", "0.00", ""], ["2163", "BENIGN NEOPLASM SKIN OF OTHER AND UNSPECIFIED PARTS OF FACE", "M", "0", "0", "0", "0", "0", "0", "0.00", ""], ["", "", "F", "0", "0", "1", "0", "0", "1", "0.41", ""], ["ENDOCRINE, NUTRITIONAL, METABOLIC &amp; IMMUNITY DISORDERS(2400-2799)", "", "", "", "5", "4", "6", "3", "7", "25", "10.20"], ["243", "CONGENITAL HYPOTHYROIDISM", "M", "0", "0", "0", "1", "0", "1", "0.41", ""], ["", "", "F", "3", "3", "2", "0", "1", "9", "3.67", ""], ["2532", "PANHYPOPITUATURISM", "M", "0", "0", "0", "0", "1", "1", "0.41", ""], ["", "", "F", "0", "0", "0", "0", "0", "0", "0.00", ""], ["2552", "CONGENITAL ADRENAL HYPERPLASIA", "M", "0", "0", "0", "0", "0", "0", "0.41", ""], ["", "", "F", "1", "0", "0", "0", "0", "1", "0.41", ""], ["2598", "OTHER ENDOCRINE DISORDERS NEC", "M", "0", "1", "0", "0", "0", "0", "0.00", ""], ["", "", "F", "0", "1", "0", "0", "0", "1", "0.41", ""], ["2701", "PHENYLKETUNURIA", "M", "0", "0", "2", "0", "1", "3", "1.22", ""], ["", "", "F", "0", "0", "0", "0", "0", "0", "0.00", ""], ["2754", "DISORDERS OF CALCIUM METABOLISM", "M", "0", "0", "1", "0", "1", "2", "0.82", ""], ["", "", "F", "0", "0", "0", "0", "0", "0", "0.00", ""], ["2762", "ACIDOSIS", "M", "0", "0", "0", "0", "0", "0", "0.00", ""], ["", "", "F", "0", "0", "0", "0", "1", "1", "0.41", ""], ["2774", "DISORDERS OF BILIUREDIN EXCRETION", "M", "0", "0", "0", "0", "1", "1", "0.41", ""], ["", "", "F", "0", "0", "0", "0", "0", "0", "0.00", ""], ["2778", "OTHER SPECIFIED DISORDERS OF METABOLISM", "M", "0", "0", "1", "1", "0", "1", "0.41", ""], ["", "", "F", "1", "0", "0", "0", "0", "0", "0.82", ""], ["2779", "UNSPECIFIED DISORDERS OF METABOLISM", "M", "1", "0", "0", "0", "0", "1", "0.41", ""], ["", "", "F", "0", "0", "0", "0", "0", "0", "0.00", ""], ["2790", "DEFICIENCY OF HUMORAL COMMUNITY", "M", "0", "0", "0", "0", "0", "0", "0.00", ""], ["", "", "F", "0", "0", "0", "0", "1", "1", "0.41", ""]]}, {"caption": "Table 17: All anomalies registered in Malta from 1993-1997 (as at December 1999) (5)", "header": ["CODE", "TEXT", "SEX", "1993", "1994", "1995", "1996", "1997", "93.97", "Prev./10000"], "rows": [["CONDITIONS OF BLOOD AND BLOOD FORMING OR GANS(2800-2099)", "", "", "0", "0", "1", "0", "1", "2", "0.82"], ["2820", "HEREDITARY SPHEROCYTOIS", "M", "0", "0", "0", "0", "1", "1", "0.41"], ["2820", "HEREDITARY SPHEROCYTOIS", "F", "0", "0", "0", "0", "0", "0", "0.00"], ["2822", "ANAEMIA DUE TO DISORDERS OF GLUTATHIONE METABOLISM", "M", "0", "0", "1", "0", "0", "1", "0.41"], ["2822", "ANAEMIA DUE TO DISORDERS OF GLUTATHIONE METABOLISM", "F", "0", "0", "0", "0", "0", "0", "0.00"], ["CONDITIONS OF NERVOUS SYSTEM AND SENSE OR GANS(1200-3899)", "", "", "3", "2", "1", "2", "1", "9", "3.67"], ["3301", "CEREBERAL LDIDOSIS INCLUDING GANGLIOSIS", "M", "2", "0", "0", "0", "1", "3", "1.22"], ["3301", "CEREBERAL LDIDOSIS INCLUDING GANGLIOSIS", "F", "0", "0", "0", "0", "0", "0", "0.00"], ["3309", "CEREBERAL DEFERENCE, UNSPECIFIED", "M", "0", "0", "0", "0", "0", "0", "0.00"], ["3309", "CEREBERAL DEFERENCE, UNSPECIFIED", "F", "1", "0", "0", "0", "0", "1", "0.41"], ["3330", "WEKDINIG HOFFMANN DISEASE INFANTILE SPINAL MUSCULAR ATROPHY", "M", "0", "0", "0", "0", "0", "0", "0.00"], ["3330", "WEKDINIG HOFFMANN DISEASE INFANTILE SPINAL MUSCULAR ATROPHY", "F", "0", "1", "0", "0", "0", "1", "0.41"], ["3331", "SPINAL MUSCULAR ATROPHY", "M", "0", "0", "0", "1", "0", "1", "0.41"], ["3331", "SPINAL MUSCULAR ATROPHY", "F", "0", "0", "0", "1", "0", "1", "0.41"], ["3992", "MYOTONIC DISORDERS", "M", "0", "0", "0", "0", "0", "0", "0.00"], ["3992", "MYOTONIC DISORDERS", "F", "0", "1", "0", "0", "0", "1", "0.41"], ["3780", "CONVEGENT CONCOMITANT STRAIRSMTS", "M", "0", "0", "1", "0", "0", "1", "0.41"], ["3780", "CONVEGENT CONCOMITANT STRAIRSMTS", "F", "0", "0", "0", "0", "0", "0", "0.00"], ["4251", "HYPERTROPHIC OBSTRUCTIVE CARDIOMYOPATHY", "", "1", "0", "2", "2", "3", "8", "3.26"], ["4251", "HYPERTROPHIC OBSTRUCTIVE CARDIOMYOPATHY", "M", "0", "0", "0", "2", "2", "4", "1.63"], ["4253", "ENDOGARDIAL FIBROELASTOIS", "", "F", "0", "1", "0", "1", "2", "0.82"], ["4253", "ENDOGARDIAL FIBROELASTOIS", "M", "0", "0", "0", "0", "0", "0", "0.00"], ["4270", "PAROXYSMAL SUPRAVENTECULAR TACHYCAORDIA", "", "F", "0", "1", "0", "0", "1", "0.41"], ["4270", "PAROXYSMAL SUPRAVENTECULAR TACHYCAORDIA", "", "F", "0", "0", "0", "0", "0", "0.00"], ["CONDITIONS OF THE DIGESTIVE SYSTEM(5200-5799)", "", "", "2", "3", "2", "2", "2", "11", "4.49"], ["5240", "MAJOR ANOMALIES OF JAW SIZE", "", "M", "1", "2", "1", "0", "2", "6.45"], ["5240", "MAJOR ANOMALIES OF JAW SIZE", "", "F", "1", "0", "0", "2", "0", "1.22"], ["550", "INGUINAL HERnia", "", "M", "0", "1", "0", "0", "0", "0.41"], ["550", "INGUINAL HERnia", "", "F", "0", "1", "0", "0", "1", "0.41"]]}, {"caption": "Table 28: Department of Health Information", "header": ["CODE", "TEXT", "SEX", "1993", "1994", "1995", "1996", "1997", "93-97", "Prev./10000"], "rows": [["CONDITIONS ORIGINATING IN THE PERINATAL PERIOD(7600-7799)", "", "", "0", "0", "2", "0", "1", "3", "1.22"], ["7710", "CONGENITAL RUBELLA", "M", "0", "0", "1", "0", "0", "1", "0.41"], ["7710", "", "F", "0", "0", "1", "0", "0", "1", "0.41"], ["7786", "CONGENITAL HYDROCELE", "M", "0", "0", "0", "0", "1", "1", "0.41"], ["7786", "", "F", "0", "0", "0", "0", "0", "0", "0.00"], ["GRAND TOTAL", "", "", "257", "317", "280", "285", "297", "1436", "585.88"]]}, {"caption": "Table 29: EUROCAT Sub groups (Annex 3) / ICD-9 code by CONGENITAL ANOMALIES, Number Malta, Prevalence/10,000 total births", "header": ["EUROCAT Sub groups (Annex 3) / ICD-9 code", "CONGENITAL ANOMALIES", "Number Malta", "Prevalence/10,000 total births", "", "Number Malta", "Prevalence/10,000 live births", ""], "rows": [["EUROCAT Sub groups (Annex 3) / ICD-9 code", "CONGENITAL ANOMALIES", "Number Malta", "Malta", "EUROCAT registries", "Number Malta", "Malta", "EUROCAT registries with preg. termination"], ["01", "Neural Tube defects*", "33", "13.5", "(5.6 - 15.9)", "28", "11.5", "(1.3 - 7.3)"], ["02-04", "Other anom alies of the Nervous System *", "46", "18.8", "(3.9 - 19.8)", "39", "16", "(4.6 - 12.9)"], ["05", "Anomalies of the eye", "15", "6.1", "(2.7 - 11.8)", "14", "5.7", "(2.4 - 11.4)"], ["06", "Anomalies of the ear", "31", "12.6", "(2.1 - 12.5)", "28", "11.5", "(2.0 - 11.5)"], ["07-09", "Congenital Heart Disease**", "513", "209.3", "(23.5 - 101.5)", "506", "207.7", "(22.1 - 93.7)"], ["ICD-7467", "Hypoplasia left heart***", "3", "1.2", "(1.5 - 3.8)", "2", "0.8", "(0.9 - 3.1)"], ["ICD-7450", "Common Truncus", "1", "0.4", "(0.2 - 3.1)", "1", "0.4", "(0.1 - 2.1)"], ["ICD-7451", "Transposition of great arteries", "11", "4.5", "(1.0 - 6.0)", "11", "4.5", "(0.9 - 5.4)"], ["10", "Respiratory System defects (excluding nose)", "24", "9.8", "NA", "23", "9.4", "NA"], ["ICD-7490", "Cleft palate**", "36", "14.7", "(2.5 - 9.4)", "36", "14.8", "(2.1 - 7.9)"], ["ICD-74912", "Cleft lip with or without palate", "21", "8.6", "(3.3 - 15.3)", "20", "8.2", "(2.7 - 14.4)"], ["12-14 excl 7505", "Anomalies of digestive system excl. pyloric stenosis", "33", "13.5", "(3.6 - 24.3)", "32", "13.1", "(2.8 - 18.8)"], ["ICD-7505", "Pyloric stenosis", "30", "12.2", "(0.6 - 47.8)", "30", "12.3", "(1.2 - 47.5)"], ["15-16", "Anomalies of external genitals", "74", "30.2", "(7.5 - 32.7)", "72", "29.6", "(7.1 - 31.1)"], ["ICD-75260", "Hypospadias (excl. glandular/oronal)", "29", "11.8", "(6.1 - 27.8)", "29", "11.9", "(6.0 - 27.3)"], ["17-19", "Anomalies of the internal urogenital system", "91", "37.1", "(6.9 - 66.5)", "88", "36.1", "(5.4 - 52.9)"], ["20-23", "Limb defects", "196", "80", "(24.8 - 89.2)", "185", "75.9", "(21.5 - 77.0)"], ["24-25", "Other musculoskeletal &amp; connective tissue defects*", "90", "36.7", "(6.8 - 34.1)", "80", "32.8", "(6.2 - 26.7)"], ["ICD-7566", "Anomalies of diaphragm*", "15", "6.1", "(1.6 - 5.8)", "15", "6.2", "(1.3 - 4.3)"], ["ICD-75670", "Omphalocele", "8", "3.3", "(0.8 - 3.9)", "5", "2.1", "(0.6 - 2.3)"], ["ICD-75671", "Gastrochisis", "3", "1.2", "(0.3 - 2.3)", "3", "1.2", "(0.2 - 1.7)"], ["30-31", "Anomalies of integument &amp; skin", "46", "18.8", "NA", "46", "18.9", "NA"], ["32", "Down Syndrome*", "41", "16.7", "(11.5 - 28.0)", "41", "16.8", "(7.5 - 12.5)"], ["33", "Other chromosomal anomalies, excl. Down syndrome*", "19", "7.8", "(6.0 - 24.6)", "19", "7.8", "(3.3 - 7.4)"], ["34-38", "Other anom alies", "65", "26.5", "NA", "62", "25.4", "NA"]]}, {"caption": "Table 30: Locality by PREVALENCE/10,000BIRTHS", "header": ["Locality", "PREVALENCE/10,000BIRTHS", "", "", "", "", ""], "rows": [["Locality", "1993", "1994", "1995", "1996", "1997", "1993-97(95%CI)"], ["North West", "18.8", "15.8", "24.3", "22.3", "7.5", "17.7(11.5-27.0)"], ["Anomalies", "5", "4", "6", "6", "2", "23"], ["Total births", "2656", "2531", "2467", "2694", "2662", "13010"], ["South East", "4.8", "15.3", "5.5", "5.1", "15.8", "9.2(4.5-18.2)"], ["Anomalies", "1", "3", "1", "1", "3", "9"], ["Total births", "2102", "1955", "1822", "1957", "1896", "9732"], ["Gozo", "0.0", "0.0", "0.0", "30.6", "0.0", "5.7(0.0-36.7)"], ["Anomalies", "0", "0", "0", "1", "0", "1"], ["Total births", "414", "377", "344", "327", "306", "1768"], ["Malta &amp; Gozo", "11.6", "14.4", "15.1", "16.1", "10.3", "13.5(9.4-19.1)"]]}, {"caption": "Table 20: Time trend of total prevalence of NTDs Malta and EUROCAT average compared", "header": ["Prevalence/10,000", "1993", "1994", "1995", "1996", "1997", "Total"], "rows": [["Malta", "11.6", "14.4", "15.1", "16.1", "10.3", "13.5(1993-97)"], ["EUROCAT average*", "9.1", "9.3", "", "", "", "14.7(1980-94)"]]}, {"caption": "Table 32: Locality by PREVALENCE/10,000 BIRTHS", "header": ["Locality", "PREVALENCE/10,000 BIRTHS", "", "", "", "", ""], "rows": [["Locality", "1993", "1994", "1995", "1996", "1997", "1993-97(95%CI)"], ["North West", "3.8", "15.8", "16.2", "3.7", "3.7", "8.5(4.5-15.6)"], ["Anomalies", "1", "4", "4", "1", "1", "11"], ["Total births", "2656", "2531", "2467", "2694", "2662", "13010"], ["South East", "14.3", "5.1", "5.5", "5.1", "5.3", "7.2(3.2-15.5)"], ["Anomalies", "3", "1", "1", "1", "1", "7"], ["Total births", "2102", "1955", "1822", "1957", "1896", "9732"], ["Gozo", "24.2", "0.0", "0.0", "0.0", "65.4", "17.0(4.4-53.9)"], ["Anomalies", "1", "0", "0", "0", "2", "3"], ["Total births", "414", "377", "344", "327", "306", "1768"], ["Malta &amp; Gozo", "9.7", "10.3", "10.8", "4.0", "8.2", "8.6(5.4-13.3)"]]}, {"caption": "Table 33: Prevalence/10,000 by Total, 1993\u20131997", "header": ["Prevalence/10,000", "1993", "1994", "1995", "1996", "1997", "Total"], "rows": [["Malta", "9.7", "10.3", "10.8", "4.0", "8.2", "8.6(1993-97)"], ["EUROCAT average*", "8.1", "9.5", "-", "-", "-", "9.0(1980-94)"]]}, {"caption": "Table 23: Distribution of Cleft Palate according to locality of residence of mother", "header": ["Locality", "PREVALENCE/10,000 BIRTHS", "", "", "", "", ""], "rows": [["Locality", "1993", "1994", "1995", "1996", "1997", "1993-97(95%CI)"], ["North West", "11.3", "4.0", "20.3", "7.4", "18.8", "12.3(7.3-20.4)"], ["Anomalies", "3", "1", "5", "2", "5", "16"], ["Total births", "2656", "2531", "2467", "2694", "2662", "13010"], ["South East", "19.0", "30.7", "5.5", "15.3", "10.6", "16.4(9.7-27.3)"], ["Anomalies", "4", "6", "1", "3", "2", "16"], ["Total births", "2102", "1955", "1822", "1957", "1896", "9732"], ["Gozo", "24.2", "0.0", "29.1", "61.2", "0.0", "22.6(7.3-62.1)"], ["Anomalies", "1", "0", "1", "2", "0", "4"], ["Total births", "414", "377", "344", "327", "306", "1768"], ["Malta &amp; Gozo", "15.5", "14.4", "15.1", "14.1", "14.9", "14.7(10.4-10.6)"]]}, {"caption": "Table 35: Prevalence/10,000 by Total, 1993\u20131997", "header": ["Prevalence/10,000", "1993", "1994", "1995", "1996", "1997", "Total"], "rows": [["Malta", "15.5", "14.4", "15.1", "14.1", "14.9", "14.7(1993-97)"], ["EUROCAT average*", "6.0", "6.7", "", "", "", "6.5(1980-94)"]]}, {"caption": "Table 36: Locality by PREVALENCE/10,000 BIRTHS", "header": ["Locality", "PREVALENCE/10,000 BIRTHS", "", "", "", "", ""], "rows": [["Locality", "1993", "1994", "1995", "1996", "1997", "1993-97(95%CI)"], ["North West", "113.0", "225.2", "174.3", "274.7", "202.9", "198.3(175-224)"], ["Anomalies", "30", "57", "43", "74", "54", "258"], ["Total births", "2656", "2531", "2467", "2694", "2662", "13010"], ["South East", "180.8", "230.2", "181.1", "178.8", "247.9", "203.5(177-234)"], ["Anomalies", "38", "45", "33", "35", "47", "198"], ["Total births", "2102", "1955", "1822", "1957", "1896", "9732"], ["Gozo", "217.4", "291.8", "290.7", "458.7", "392.2", "322.4(247-419)"], ["Anomalies", "9", "11", "10", "15", "12", "57"], ["Total births", "414", "377", "344", "327", "306", "1768"], ["Malta &amp; Gozo", "148.9", "232.4", "185.6", "249.1", "232.3", "209.3(194-231)"]]}, {"caption": "Table 37: Prevalence/10,000 by Total, 1993\u20131997", "header": ["Prevalence/10,000", "1993", "1994", "1995", "1996", "1997", "Total"], "rows": [["Malta", "149", "232", "186", "249", "232", "209(1993-97)"], ["EUROCAT average*", "66", "60", "", "", "", "54(1980-94)"]]}, {"caption": "Table 38: Locality by PREVALENCE/10,000BIRTHS", "header": ["Locality", "PREVALENCE/10,000BIRTHS", "", "", "", "", ""], "rows": [["Locality", "1993", "1994", "1995", "1996", "1997", "1993-97(95%CI)"], ["North West", "11.3", "4.0", "16.2", "26.0", "11.3", "13.8(8.5-22.3)"], ["Anomalies", "3", "1", "4", "7", "3", "18"], ["Total births", "2656", "2531", "2467", "2694", "2662", "13010"], ["South East", "14.3", "15.3", "27.4", "10.2", "10.6", "15.4(9.0-26.1)"], ["Anomalies", "3", "3", "5", "2", "2", "15"], ["Total births", "2102", "1955", "1822", "1957", "1896", "9732"], ["Gozo", "0.0", "0.0", "0.0", "0.0", "0.0", "0.0(0.0-27.0)"], ["Anomalies", "0", "0", "0", "0", "0", "0"], ["Total births", "414", "377", "344", "327", "306", "1768"], ["Malta &amp; Gozo", "12.2", "8.2", "19.4", "18.1", "10.3", "13.5(9.4-19.1)"]]}, {"caption": "Table 39: Prevalence/10,000 by Total, 1993\u20131997", "header": ["Prevalence/10,000", "1993", "1994", "1995", "1996", "1997", "Total"], "rows": [["Malta", "12.2", "8.2", "19.4", "18.1", "10.3", "13.5(1993-97)"], ["EUROCAT average*", "13.8", "13.5", "", "", "", "14.3(1980-94)"]]}, {"caption": "Table 40: Locality by PREVALENCE/10,000 BIRTHS", "header": ["Locality", "PREVALENCE/10,000 BIRTHS", "", "", "", "", ""], "rows": [["Locality", "1993", "1994", "1995", "1996", "1997", "1993-97(95%CI)"], ["North West", "0.0", "15.8", "8.1", "3.7", "37.6", "13.1(7.9-21.4)"], ["Anomalies", "0", "4", "2", "1", "10", "17"], ["Total births", "2656", "2531", "2467", "2694", "2662", "13010"], ["South East", "14.3", "15.3", "5.5", "5.1", "15.8", "11.3(5.9-20.9)"], ["Anomalies", "3", "3", "1", "1", "3", "11"], ["Total births", "2102", "1955", "1822", "1957", "1896", "9732"], ["Gozo", "0.0", "53.1", "0.0", "0.0", "0.0", "11.3(1.9-45.5)"], ["Anomalies", "0", "2", "0", "0", "0", "2"], ["Total births", "414", "377", "344", "327", "306", "1768"], ["Malta &amp; Gozo", "5.8", "18.5", "6.5", "4.0", "26.7", "12.2(8.4-17.7)"]]}, {"caption": "Table 41: Prevalence/10,000 by Total, 1993\u20131997", "header": ["Prevalence/10,000", "1993", "1994", "1995", "1996", "1997", "Total"], "rows": [["Malta", "5.8", "18.5", "6.5", "4.0", "26.7", "12.2(1993-97)"], ["EUROCAT average*", "6.7", "5.7", "", "", "", "7.5(1980-94)"]]}, {"caption": "Table 42: Locality by PREVALENCE/10,000 BIRTHS", "header": ["Locality", "PREVALENCE/10,000 BIRTHS", "", "", "", "", ""], "rows": [["Locality", "1993", "1994", "1995", "1996", "1997", "1993-97(95%CI)"], ["North West", "3.8", "0.0", "8.1", "11.1", "3.8", "5.4(2.4-11.6)"], ["Anomalies", "1", "0", "2", "3", "1", "7"], ["Total births", "2656", "2531", "2467", "2694", "2662", "13010"], ["South East", "9.5", "0.0", "5.5", "5.1", "0.0", "4.1(1.3-11.3)"], ["Anomalies", "2", "0", "1", "1", "0", "4"], ["Total births", "2102", "1955", "1822", "1957", "1896", "9732"], ["Gozo", "0.0", "0.0", "0.0", "0.0", "0.0", "0.0(0.0-27.0)"], ["Anomalies", "0", "0", "0", "0", "0", "0"], ["Total births", "414", "377", "344", "327", "306", "1768"], ["Malta &amp; Gozo", "5.8", "0.0", "6.5", "8.0", "2.1", "4.5(2.4-8.3)"]]}, {"caption": "Table 43: Prevalence/10,000 by Total, 1993\u20131997", "header": ["Prevalence/10,000", "1993", "1994", "1995", "1996", "1997", "Total"], "rows": [["Malta", "5.8", "0.0", "6.5", "8.0", "2.1", "4.5(1993-97)"], ["EUROCAT average*", "2.8", "2.9", "", "", "", "3.4(1980-94)"]]}, {"caption": "Table 44: Locality by PREVALENCE/10,000 BIRTHS", "header": ["Locality", "PREVALENCE/10,000 BIRTHS", "", "", "", "", ""], "rows": [["Locality", "1993", "1994", "1995", "1996", "1997", "1993-97(95%CI)"], ["North West", "67.8", "71.1", "20.3", "44.5", "33.8", "47.7(36.9-61.5)"], ["Anomalies", "18", "18", "5", "12", "9", "62"], ["Total births", "2656", "2531", "2467", "2694", "2662", "13010"], ["South East", "0.0", "35.8", "49.4", "20.4", "42.2", "28.8(19.5-42.2)"], ["Anomalies", "0", "7", "9", "4", "8", "28"], ["Total births", "2102", "1955", "1822", "1957", "1896", "9732"], ["Gozo", "0.0", "0.0", "0.0", "30.6", "0.0", "5.7(0.3-36.7)"], ["Anomalies", "0", "0", "0", "1", "0", "1"], ["Total births", "414", "377", "344", "327", "306", "1768"], ["Malta &amp; Gozo", "34.8", "51.4", "30.2", "34.2", "35.0", "37.1(30.0-45.8)"]]}, {"caption": "Table 45: Prevalence/10,000 by Total, 1993\u20131997", "header": ["Prevalence/10,000", "1993", "1994", "1995", "1996", "1997", "Total"], "rows": [["Malta", "34.8", "51.4", "30.2", "34.2", "35.0", "37.1(1993-97)"], ["EUROCAT average*", "34.6", "36.1", "", "", "", "26.1(1980-94)"]]}, {"caption": "Table 35: Distribution of cystic kidney defects according to locality of residence of mother", "header": ["Locality", "PREVALENCE/10,000 BIRTHS", "", "", "", "", ""], "rows": [["Locality", "1993", "1994", "1995", "1996", "1997", "1993-97(95%CI)"], ["North West", "7.5", "4.0", "0.0", "3.7", "7.5", "4.6(1.9-10.6)"], ["Anomalies", "2", "1", "0", "1", "2", "6"], ["Total births", "2656", "2531", "2467", "2694", "2662", "13010"], ["South East", "0.0", "10.2", "16.5", "0.0", "0.0", "5.1(1.9-12.7)"], ["Anomalies", "0", "2", "3", "0", "0", "5"], ["Total births", "2102", "1955", "1822", "1957", "1896", "9732"], ["Gozo", "0.0", "0.0", "0.0", "0.0", "0.0", "0.0(0.0-27.0)"], ["Anomalies", "0", "0", "0", "0", "0", "0"], ["Total births", "414", "377", "344", "327", "306", "1768"], ["Malta &amp; Gozo", "3.9", "6.2", "6.5", "2.0", "4.1", "4.5(2.3-8.3)"]]}, {"caption": "Table 47: Prevalence/10,000 by Total, 1993\u20131997", "header": ["Prevalence/10,000", "1993", "1994", "1995", "1996", "1997", "Total"], "rows": [["Malta", "3.9", "6.2", "6.5", "2.0", "4.1", "4.5(1993-97)"], ["EUROCAT average*", "5.0", "5.8", "", "", "", "4.1(1980-94)"]]}, {"caption": "Table 37: Distribution of limb reduction defects according to locality of residence of mother", "header": ["Locality", "PREVALENCE/10,000 BIRTHS", "", "", "", "", ""], "rows": [["Locality", "1993", "1994", "1995", "1996", "1997", "1993-97(95%CI)"], ["North West", "3.8", "7.9", "8.1", "0.0", "0.0", "3.8(1.4-9.5)"], ["Anomalies", "1", "2", "2", "0", "0", "5"], ["Total births", "2656", "2531", "2467", "2694", "2662", "13010"], ["South East", "4.8", "5.1", "16.5", "5.1", "5.3", "7.2(3.2-15.5)"], ["Anomalies", "1", "1", "3", "1", "1", "7"], ["Total births", "2102", "1955", "1822", "1957", "1896", "9732"], ["Gozo", "0.0", "0.0", "0.0", "0.0", "0.0", "0.0(0.0-27.0)"], ["Anomalies", "0", "0", "0", "0", "0", "0"], ["Total births", "414", "377", "344", "327", "306", "1768"], ["Malta &amp; Gozo", "3.9", "6.2", "10.8", "2.0", "2.1", "4.9(2.7-8.8)"]]}, {"caption": "Table 49: Prevalence/10,000 by Total, 1993\u20131997", "header": ["Prevalence/10,000", "1993", "1994", "1995", "1996", "1997", "Total"], "rows": [["Malta", "3.9", "6.2", "10.8", "2.0", "2.1", "4.9(1993-97)"], ["EUROCAT average*", "6.1", "6.2", "", "", "", "6.0(1980-94)"]]}, {"caption": "Table 50: Locality by PREVALENCE/10,000BIRTHS", "header": ["Locality", "PREVALENCE/10,000BIRTHS", "", "", "", "", ""], "rows": [["Locality", "1993", "1994", "1995", "1996", "1997", "1993-97(95%CI)"], ["North West", "30.1", "19.8", "20.3", "18.6", "22.5", "22.3(15.2-32.5)"], ["Anomalies", "8", "5", "5", "5", "6", "29"], ["Total births", "2656", "2531", "2467", "2694", "2662", "13010"], ["South East", "14.3", "20.5", "16.5", "10.2", "10.6", "14.4(8.2-24.8)"], ["Anomalies", "3", "4", "3", "2", "2", "14"], ["Total births", "2102", "1955", "1822", "1957", "1896", "9732"], ["Gozo", "0.0", "0.0", "0.0", "0.0", "0.0", "0.0(0.0-27.0)"], ["Anomalies", "0", "0", "0", "0", "0", "0"], ["Total births", "414", "377", "344", "327", "306", "1768"], ["Malta &amp; Gozo", "21.3", "18.5", "17.3", "14.1", "16.5", "17.5(12.9-23.9)"]]}, {"caption": "Table 51: Prevalence/10,000 by Total, 1993\u20131997", "header": ["Prevalence/10,000", "1993", "1994", "1995", "1996", "1997", "Total"], "rows": [["Malta", "21.3", "18.5", "17.3", "14.1", "16.5", "17.5(1993-97)"], ["EUROCAT average*", "8.2", "8.9", "", "", "", "8.3(1980-94)"]]}, {"caption": "Table 41: Distribution of syndactyly according to locality of residence of mother", "header": ["Locality", "PREVALENCE/10,000 BIRTHS", "", "", "", "", ""], "rows": [["Locality", "1993", "1994", "1995", "1996", "1997", "1993-97(95%CI)"], ["North West", "7.5", "4.0", "12.2", "0.0", "0.0", "4.6(1.9-10.6)"], ["Anomalies", "2", "1", "3", "0", "0", "6"], ["Total births", "2656", "2531", "2467", "2694", "2662", "13010"], ["South East", "14.3", "10.2", "11.0", "5.1", "21.1", "12.3(6.7-22.2)"], ["Anomalies", "3", "2", "2", "1", "4", "12"], ["Total births", "2102", "1955", "1822", "1957", "1896", "9732"], ["Gozo", "0.0", "0.0", "0.0", "61.2", "0.0", "11.3(1.2-45.5)"], ["Anomalies", "0", "0", "0", "2", "0", "2"], ["Total births", "414", "377", "344", "327", "306", "1768"], ["Malta &amp; Gozo", "9.7", "6.2", "10.8", "6.0", "8.2", "8.2(5.1-12.9)"]]}, {"caption": "Table 53: Prevalence/10,000 by Total, 1993\u20131997", "header": ["Prevalence/10,000", "1993", "1994", "1995", "1996", "1997", "Total"], "rows": [["Malta", "9.7", "6.2", "10.8", "6.0", "8.2", "8.2(1993-97)"], ["EUROCAT average*", "5.5", "5.2", "", "", "", "5.8(1980-94)"]]}, {"caption": "Table 54: Locality by PREVALENCE/10,000 BIRTHS", "header": ["Locality", "PREVALENCE/10,000 BIRTHS", "", "", "", "", ""], "rows": [["Locality", "1993", "1994", "1995", "1996", "1997", "1993-97(95%CI)"], ["North West", "0.0", "7.9", "8.1", "11.1", "7.5", "6.9(3.4-13.7)"], ["Anomalies", "0", "2", "2", "3", "2", "9"], ["Total births", "2656", "2531", "2467", "2694", "2662", "13010"], ["South East", "4.8", "5.1", "5.5", "5.1", "5.3", "5.1(1.9-12.7)"], ["Anomalies", "1", "1", "1", "1", "1", "5"], ["Total births", "2102", "1955", "1822", "1957", "1896", "9732"], ["Gozo", "24.2", "0.0", "0.0", "0.0", "0.0", "5.7(0.3-36.7)"], ["Anomalies", "1", "0", "0", "0", "0", "1"], ["Total births", "414", "377", "344", "327", "306", "1768"], ["Malta &amp; Gozo", "3.9", "6.2", "6.5", "8.0", "6.2", "6.1(3.6-10.4)"]]}, {"caption": "Table 55: Prevalence/10,000 by Total, 1993\u20131997", "header": ["Prevalence/10,000", "1993", "1994", "1995", "1996", "1997", "Total"], "rows": [["Malta", "3.9", "6.2", "6.5", "8.0", "6.2", "6.1(1993-97)"], ["EUROCAT average*", "3.6", "6.8", "", "", "", "3.4(1980-94)"]]}, {"caption": "Table 56: Maternal age groups by Total", "header": ["", "Maternal age groups", "", "", "", "", "", "", "Total"], "rows": [["", "&lt;20", "20-24", "25-29", "30-34", "35-39", "40-44", "45+", ""], ["Babies with Down syndrome", "0", "0", "3", "12", "17", "9", "0", "41"], ["Total births", "957", "4932", "8581", "6489", "2910", "602", "39", "24510"], ["Prevalence/10,000", "0.0", "0.0", "3.5", "18.5", "58.4", "149.5", "0.0", "16.7"]]}, {"caption": "Table 46: Distribution of Down syndrome according to locality of residence of mother", "header": ["Locality", "PREVALENCE/10,000 BIRTHS", "", "", "", "", ""], "rows": [["Locality", "1993", "1994", "1995", "1996", "1997", "1993-97(95%CI)"], ["North West", "22.6", "11.9", "16.2", "11.1", "7.5", "13.8(8.5-22.3)"], ["Anomalies", "6", "3", "4", "3", "2", "18"], ["Total births", "2656", "2531", "2467", "2694", "2662", "13010"], ["South East", "33.3", "15.3", "21.9", "20.4", "5.3", "19.5(12.1-31.1)"], ["Anomalies", "7", "3", "4", "4", "1", "19"], ["Total births", "2102", "1955", "1822", "1957", "1896", "9732"], ["Gozo", "48.3", "26.5", "0.0", "30.6", "0.0", "22.6(7.3-62.1)"], ["Anomalies", "2", "1", "0", "1", "0", "4"], ["Total births", "414", "377", "344", "327", "306", "1768"], ["Malta &amp; Gozo", "29.0", "14.4", "17.3", "16.1", "6.2", "16.7(12.2-22.9)"]]}, {"caption": "Table 58: Prevalence/10,000 by Total, 1993\u20131997", "header": ["Prevalence/10,000", "1993", "1994", "1995", "1996", "1997", "Total"], "rows": [["Malta", "29.0", "14.4", "17.3", "16.1", "6.2", "16.7(1993-97)"], ["EUROCAT average*", "17.8", "17.3", "", "", "", "16.1(1980-94)"]]}, {"caption": "Table 48: Prevalence of Down syndrome in Malta with maternal age under 30 years", "header": ["", "PREVALENCE/10,000 BIRTHS", "", "", "", "", ""], "rows": [["", "1993", "1994", "1995", "1996", "1997", "1993-97(95%CI)"], ["Anomalies", "1", "2", "0", "0", "0", "3"], ["Total births(&lt;30wrs)", "3030", "2806", "2658", "2981", "2995", "14470"], ["Malta &amp; Gozo", "3.3", "7.1", "0.0", "0.0", "0.0", "2.1(0.5-6.6)"]]}, {"caption": "Table 60: Malta and EUROCAT average compared", "header": ["Prevalence/10,000", "1993", "1994", "1995", "1996", "1997", "Total"], "rows": [["Malta", "3.3", "7.1", "0.0", "0.0", "0.0", "2.1(1993-97)"], ["EUROCAT average*", "8.2", "8.1", "", "", "", "7.6(1980-94)"]]}, {"caption": "Table 50: Prevalence of Down syndrome in Malta with maternal age 35 years and over", "header": ["", "PREVALENCE/10,000 BIRTHS", "", "", "", "", ""], "rows": [["", "1993", "1994", "1995", "1996", "1997", "1993-97(95%CI)"], ["Anomalies", "11", "4", "3", "6", "2", "26"], ["Total births(&gt;=35vs)", "751", "697", "680", "718", "705", "3551"], ["Malta&amp;Gozo", "146.5", "57.4", "44.1", "83.6", "28.4", "73.2(48.9-108.7)"]]}, {"caption": "Table 62: Prevalence/10,000 by Total, 1993\u20131997", "header": ["Prevalence/10,000", "1993", "1994", "1995", "1996", "1997", "Total"], "rows": [["Malta", "146.0", "57.4", "44.1", "83.6", "28.4", "73.2(1993-97)"], ["EUROCAT average*", "57.8", "62.2", "", "", "", "61.8(1980-94)"]]}, {"caption": "Annex 1 Local Report Form", "header": ["CONFIDENTIAL REPORT ON CONGENITAL ANOMALIES", "", ""], "rows": [["CHILD&#x27;S NAME:", "", "I.D."], ["ADDRESS:", "", ""], ["DATE OF BIRTH:", "", ""], ["MOTHER&#x27;S NAME:", "", "I.D."], ["DIAGNOSIS:", "", ""], ["REFERRING DOCTOR:", "", "DATE:"], ["PLEASE SEND INFORMATION TO DR. MIRIAM GATT, DEPT. OF HEALTH INFORMATION 95 G&#x27;MANGIA HILL, G&#x27;MANGIA MSD 08", "", ""]]}, {"caption": "Annex 3 Eurocat Subgroups", "header": ["EUROCAT sub group and Text", "ICD-9 codes included"], "rows": [["01 Neural Tube defects", "7400-7420"], ["02 Congenital Hydrocephaly", "7423 excl 74232"], ["03 Microcephaly", "7421,"], ["04 Other Congenital anomalies of the Nervous System", "7422,7424-5,7428-9,3440-9,3492,3519,3526,225-2375-7,2370-1,2379"], ["05 Congenital anomalies of the eye", "7430-7439,3627,3622,3743,3787,3795,224"], ["06 Congenital anomalies of the ear", "7440-7443"], ["07 Anomalies of cardiac septal closure", "7450-7459"], ["08 Other congenital anomalies of the heart", "7460-7469,4253,7852,"], ["09 Other congenital anomalies of circulatory system", "7470-6,7478,7479"], ["10 Anomalies of the Respiratory System", "7482-6,7488-9,2358,7702,4920"], ["11 Cleft lip and palate", "7490-7492"], ["12 Tracheo-oesophageal fistula, oesophageal atresia and stenosis", "75030-75038,"], ["13 Atresia and stenosis of large intestine, rectum and anal canal", "75121-75124"], ["14 Other anomalies of the digestive system and upper alimentary tract", "7504-5,7507-11,7413-9,75120,211-"], ["15 Anomalies of the external genital organs(male)", "7525-6,7528,7786"], ["16 Anomalies of external female genitalia and indeterminate sex", "7524,7527"], ["17 Other anomalies of genital organs", "7520-3,7529,219-,220-,221-,222-"], ["18 Renal Anom alies", "7530-1,7533,2330,"], ["19 Anomalies of urinary tract", "7532,7534-9,2231-3,2238-9"], ["20 Polydactyly and syndactyly", "7550-7551"], ["21 Reduction deformities of limbs", "7552-7554"], ["22 Talipes", "7545-7547"], ["23 Other anomalies of limbs", "7543-4,7555-6,7558-9"], ["24 Anomalies of the tongue, brachial cleft, auricular sinus", "7444,7500-2"], ["25 Anomalies of nose, face, skull and neck", "5240,5249,7445,7448-9,7480-1,7540,7560,5209"], ["26 Anomalies of the diaphragm", "7506,7566"], ["27 Other musculoskeletal anomalies of thorax and neck", "7548,7561,7541-2,7562-3"], ["28 Anomalies of the abdominal wall", "7567,5509,5530-2,5538-9"], ["29 Other anomalies of bones, muscles, cartilages and connective tissues", "7564-5,7568-9,2380"], ["30 Anomalies of the integument", "7570-2,7574-5,7578-9"], ["31 Skin tags and benign neoplasms of the skin", "6851,7573,2140,2169,2280-1"], ["32 Down Syndrome", "7580,"], ["33 Other chromosomal anomalies, Down Syndrome excluded", "7581-9"], ["34 Metabolic defects", "2439,2461,2533-4,2552,2579,2598,2700-112718-33,2738-41,2748-54,2758-59,2770-6,2778-79,2820-7,2860-3"], ["35 Anomalies of breast, spleen, adrenal gland and other endocrine glands", "7576,7590-2"], ["36 Other syndromes, eponyms and disease names", "2873,2879,7593-6,7598,7602,7710-2,0900,8888,7726"], ["37 Other unspecified and ill-defined conditions", "7599,7597,7780"], ["38 Other", "Conditions NEC"]]}, {"caption": "Annex 4 Eurocat Report Form", "header": ["INFANT", "", "MOTHER", "", "DIAGNOSIS - MALFORMATIONS", ""], "rows": [["Local ID No.", "", "Resistance code", "Date of birth", "Syndrome", ""], ["Date of Birth", "", "Age at delivery (years)", "", "Malformations process", ""], ["Place of Birth", "", "Reproductive history", "", "", ""], ["Sex", "0=male 1=female", "Prev. spontaneous abortion", "1st", "1.", ""], ["No.of babies delivered", "", "Prev. induced abortion", "1st", "2.", ""], ["Birth order (in multiple set)", "", "Prev. live birth", "1st", "3.", ""], ["No.malformed(in multiple set)", "", "Prev.suffered(1)st", "", "4.", ""], ["Type of Birth", "(1-2=preterm)(2-3=neonatal)(4-5=autonomic)(6-7=septic) (8-9=complicated)", "Total Prev. pregnancy", "1st", "5.", ""], ["Birth weight(gms)", "", "Occupation", "", "6.", ""], ["Date of LMP, and Certainty", "", "Social status", "", "7.", ""], ["Length of gestation(cm)", "", "Race type", "", "8.", ""], ["Date of death", "", "Assisted conception", "", "", ""], ["Survival key,a work of age", "(1-2=preterm)(3-4=neonatal)(5-6=autonomic)(7-8=complicated)", "Illness before pregnancy", "", "", ""], ["Sources of information", "", "Illness during pregnancy", "", "", ""], ["DIAGNOSIS-TIME AND PROCESS", "", "Habitat expenses*", "", "", ""], ["Date of discovery", "", "(specify)", "", "", ""], ["If prenally diagnosed,part. age at discovery", "", "Urinal exposure(specify)", "", "", ""], ["Cradiation at discovery", "", "Drugs(1st trim)1.", "", "", ""], ["Prenatal diagnosis", "", "2.", "", "", ""], ["Ambiosis/osis", "", "3.", "", "", ""], ["Ubrassard", "", "RATHER", "", "", ""], ["Coccinial Vill sampling", "", "Date of birth", "", "1.", ""], ["Other techniques(specific)", "", "Age at delivery(years)", "", "2.", ""], ["Karyotype of infant/female(specific)", "", "Occupation", "", "3.", ""], ["Post-mortem examination", "", "Race type", "", "Family history of mortality", ""], ["", "", "Chronic illnesses", "", "Sites with sorbidity(*Specify)"]]}, {"caption": "Table 66: North-West group of regions", "header": ["North-West group of regions", "", "", "", ""], "rows": [["West", "North", "Central", "Central North", "Central West"], ["Zebbug", "Mellieha", "Hamrun", "Sliema", "Attard"], ["Siggiewi", "Mgarr", "Sta Venera", "St. Julian&#x27;s", "Balzan"], ["Mdina", "St Paul", "Msida/G&#x27;Mangia/Fieta", "San Gwann", "Birkirkara"], ["Dingli", "Gharghur", "Gzira/Ta&#x27;Xbiex", "", "Lija/Iklin"], ["Rabat", "Mosta"]]}]}